Prosthetic rehabilitation of a patient with Type-I ectodermal dysplasia: A case report

Abstract

Type-I ectodermal dysplasia (Christ-Siemens-Touraine syndrome) is characterized by clinical triad of hypohidrosis, hypotrichosis, and hypodontia or anodontia. Depending on the severity of the condition, various prosthodontic treatments are recommended to re-establish the masticatory function, appearance, speech, and also to improve the emotional and social aspects of the child. The various treatments may include removable partial/complete prosthesis, fixed and/or implant-supported prosthesis, or a combination of these. In this clinical report, an 11 year old girl is presented with hypohidrotic ectodermal dysplasia. Implant-supported restorations can improve the physiologic and psychosocial function, when compared with removable dentures; but their placement in growing jaws can cause complications. So, a maxillary flexible removable partial denture and a mandibular conventional complete denture with neutral zone technique were fabricated after considering her growth and the number and condition of her present teeth. Composite resin material was used to restore the conical maxillary canine for a favorable aesthetic appearance.